congenital self healing cutaneous langerhans cell histiocytosis with multiple hypopigmented macules after recovery in a neonate

نویسندگان

a. ramyar

b. yaghmaie m. monajemzadeh

چکیده

langerhans cell histiocytosis (lch) is the most common type of childhood histiocytic disorder with an incidence of 0.2 to 1 per 100,000 children under the age of 15 years (1). the clinical picture of lch varies from single system (s-s)bone or skin disease to multi-system disease (m-s) (2). we report a neonate with disseminated papulonodular eruption containing mononuclear cd1a and s100 positive histiocytic cells infiltration at epidermis and underlying dermis. the diagnosis of a congenital self healing langerhans cell histiocytosis (cshlch) was made and follow up showed a complete recovery of the eruptions , leaving hypopigmented macules in the sites corresponding to the initial findings.

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عنوان ژورنال:
acta medica iranica

جلد ۴۶، شماره ۱، صفحات ۸۴-۸۶

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